Abstract Amyloidosis is a disease caused by extracellular deposition of insoluble protein fibrils, that results in changes in tissue architecture and consequently modification of the organ structure. Cardiac involvement is common in amyloidosis. Two major types of systemic amyloidosis affect the myocardium – immunoglobulin light chain and transthyretin amyloidosis – each leading to different prognosis. Early detection and diagnosis of cardiac amyloidosis are the main objectives in the assessment of the disease. New techniques of magnetic resonance imaging have minimized […]

Abstract Arrhythmogenic right ventricular dysplasia is a classic form of chronic myocardial disease with a broad phenotypical spectrum. We report an atypical case of a patient with biventricular arrhythmogenic cardiomyopathy. Although the current diagnosis criteria are the most widely accepted ones, they focus solely on the right ventricular phenotype. The use of late gadolinium enhancement in cardiac magnetic resonance in this patient was essential for the diagnosis and assessment of the left ventricular involvement extent. This tool allows a broader […]

Introdução A calcificação do anel mitral (CAM) é definida como uma degeneração crônica do anel fibroso da valva mitral envolvendo principalmente o anel posterior. É uma condição comum em idosos, especialmente em mulheres, e está associada à hipertensão arterial sistêmica. A necrose caseosa da valva mitral (NCVM) é uma variante rara e menos conhecida da CAM, com prevalência de 0,64%, podendo chegar até 2,7% em estudo de necropsia de pacientes com CAM.– A NCVM apresenta-se à ecocardiografia como uma grande […]